Renal Papillary Necrosis Caused by Protein C Deficiency Leading to Recurrent Hydronephrosis
نویسندگان
چکیده
A patient with history of a solitary functioning kidney and protein C deficiency (PCD) presented with recurrent severe hydronephrosis causing acute kidney injury upon chronic kidney disease. Work-up with endoscopic evaluation revealed renal papillary necrosis (RPN) and sloughed renal papillae to be the true cause of the recurrent obstruction. Pathologic evaluation of the sloughed tissue confirmed the diagnosis of RPN. This is the first case reported in the literature illustrating the unique presentation of RPN in the setting of PCD.
منابع مشابه
Case Reports PAPILLARY RENAL CARCINOMA PRESENTING AS HYDRONEPHROSIS
OBJECTIVE: We describe a new case of incidental renal papillary carcinoma. We perform a bibliogra-phic review. METHODS: The papillary renal cell carcinoma is a variant of renal carcinoma. They classify in two subtypes that have relation with their prognosis. We presented one case of re-nal papillary carcinoma in a male of 76 years, play-acting as severe hydronephrosis. RESULTS/DISCUSSION: We de...
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